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. Author manuscript; available in PMC: 2007 Nov 21.
Published in final edited form as: Mol Genet Metab. 2007 Jun 18;92(1-2):160–167. doi: 10.1016/j.ymgme.2007.05.004

Table 1.

Study Cohort Characteristics.

% Femalea 50%
Average Age at time of Testa 46.5 (range 1–73y)
% ESRDa,b 20.7%
Average GFR (ml/min)c 68.7 (range 14–126)
% Liver cystsa 74.3%
% Vascular complicationsa 9.8%
% Unknown or no Family Historya 28%
a

Data available for N=82 subjects.

b

ESRD defined as transplant, dialysis or MDRD (Modification of Diet in Renal Disease) GFR <10.

c

Data available for 80 patients.