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. 2007 Nov;62(11):1008–1012. doi: 10.1136/thx.2004.031039

Table 1 Histological and clinical classification of idiopathic interstitial pneumonias*.

Histological patterns Clinical/radiological/pathological diagnosis
Usual interstitial pneumonia Idiopathic pulmonary fibrosis/cryptogenic fibrosing alveolitis
Non‐specific interstitial pneumonia Non‐specific interstitial pneumonia (provisional)†
Organising pneumonia Cryptogenic organising pneumonia‡
Diffuse alveolar damage Acute interstitial pneumonia
Respiratory bronchiolitis Respiratory bronchiolitis interstitial lung disease
Desquamative interstitial pneumonia Desquamative interstitial pneumonia
Lymphoid interstitial pneumonia Lymphoid interstitial pneumonia

*Unclassifiable interstitial pneumonia: some cases are unclassifiable for a variety of reasons.

†A heterogeneous group with poorly characterised clinical and radiological features that needs further study.

‡Cryptogenic organising pneumonia is the preferred term but it is synonymous with idiopathic bronchiolitis obliterans organising pneumonia.

Reproduced with permission from the American Thoracic Society/European Respiratory Society.1