Table 1.

Therapeutic options: an overview of the literature

Author	PY	N	Treatment	Outcome
Hamilton et al. [24]	1993	3	Corticosteroid + Aza (N = 2)	Remission with after addition Aza
			Mtx + chloroquine (N = 1)	No improvement with Mtx
				Remission after addition chloroquine
Masson et al. [25]	1993	7	Corticosteroid (N = 4)	Improvement but corticodependent
			Radiotherapy (N = 1)	No lasting improvement
			Corticotherapy + Aza (N = 1)	Permitting lowering of corticotherapy after introduction of Aza
Botella et al. [26]	1994	1	Surgery	Temporary relief
Parney et al. [11]	1997	1	Antituberculous therapy	Total remission
Nishioka et al. [27]	1998	1	Corticotherapy	Relapse
Hatano et al. [23]	1999	6	Corticotherapy (N = 4)	Three sustained remissions
			Surgery + corticotherapy (N = 1)	Three relapses
			Corticotherapy + cyclophosphamide (N = 1)
Yamamoto et al. [28]	2000	1	Corticotherapy	Remission after lymphocytapheresis
			Lymphocytapheresis
Dumont et al. [29]	2000	2	One corticotherapy	Sustained remission
			One surgery	Sustained remission
Sylaja et al. [3]	2002	4	Four corticotherapy	One complete remission
				Three partial remission
Lee et al. [5]	2003	1	Surgery	Remission
Riku et al. [12]	2003	14	Thirteen corticotherapy	Relapses in 7 patients
			One corticotherapy + Aza	Long-term improvement
			One surgery
Kupersmith et al. [10]	2004	12	Twelve corticotherapy	Relapses in 6 patients
			Two corticotherapy + Mtx	Reduction of corticotherapy
			Two corticotherapy + Aza	Reduction of corticotherapy
Rossi et al. [30]	2004	4	Corticotherapy	Three remission
				One relapse
Kanemoto et al. [31]	2005	1	Corticotherapy	Remission
Ruiz et al. [32]	2006	1	Subcutanous methotrexate	Total remission
Rudnik et al. [33]	2007	1	Corticotherapy	Remission

PY publication year, N number of patients, Aza azathioprine, Mtx methotrexate