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. 2008 Apr 24;14:750–755.

Table 1. Clinical features of affected family members.

Number
Age
Gender
Onset age
Surgery age
Clinical features
II1
73
Female
20
30
Aphakia, after cataract surgery
II3
61
Male
14–15
30
Aphakia, after cataract surgery
III1
53
Male
30

Bilateral coronary,punctate, asteroidal (above the posterior pole) cataracts
III2
50
Male
20

Bilateral coronary, punctate cataracts; gray opacity in partial coronary area
III3
42
Female
15
25
Aphakia, after cataract surgery
III4
47
Female
16–17
32
Right coronary, punctate, asteroidal (posterior pole) cataracts; left after cataract surgery
III5
36
Female
14–15
27
Aphakia, after cataract surgery
III20
40
Female
13
22
After bilateral phacoemulsification and intraocular lens implantation
III21
37
Female
10
29
After bialateral phacoemulsification and intraocular lens implantation
III22
35
Male
12

Bilateral punctate, asteroidal (above the posterior pole) cataracts
III23
33
Male
12
33
Proband
IV1
25
Male
12

Bilateral punctate, asteroidal (above the posterior pole) cataracts
IV4
22
Female
12

Bilateral punctate, asteroidal (above the posterior pole) cataracts
IV8
19
Male
10

Bilateral coronary, punctate cataracts
IV10
24
Female
15

Bilateral coronary, inverted T-shaped (posterior pole) cataracts
IV15
13
Male


Bilateral sparse punctate, asteroidal (above the posterior pole) cataracts
IV16 6 Male Sparse punctate opacities

Before the age of 10, no clinical features were manifest (IV16); punctate opacification was primarily scattered in the lens perimeter, causing almost no influence on the life of the affected individuals. In adolescence, affected individuals showed ambiguous visual clinical features. At about the age of 30, the clinical features became serious. Two affected family members (III4, III23) had different clinical features between their two lenses; III1, III2, III22, and IV10 had different clinical features from each other. The clinical features of III22, IV1, and IV4 were similar.