Table 2. Management strategy and outcome.
| Case no. | Primary management | Secondary management | Outcome |
|---|---|---|---|
| 1 | Tumour resection (ex situ) | Elective post-resection chemotherapya | Alive and disease free, 3 years after diagnosis |
| 2 | Total hepatectomy (transplant) | CMV pneumonia, death 2 months after transplant | |
| 3 | Total hepatectomy (transplant) | Recurrence at 3 months → chemotherapya | Recurrence, death 5 months after transplant |
| 4 | Chemotherapy (A)a | Rescue chemotherapy (B)a | Alive, stable disease, 2 years after diagnosis |
| 5 | Chemotherapy (A)a | Rescue chemotherapy (B)a | Alive, stable disease, 18 months after diagnosis |
Chemotherapy regimens: see Table 3.