Table 4.

FV levels in plasma and platelets, the means and the ratios between patients and healthy controls.

Patient	Plate count, ×106 plts/mL	Plasma FV, ng/mL	Plasma FV, ng/mL blood	Platelet FV, ng/109 plts	Platelet FV, ng/mL blood	Platelet FV/total FV, %
Control group
Control 1	427	7242	4251	778	332	7.2
Control 2	331	8000	4424	661	219	4.7
Control 3	186	6708	3542	545	101	2.9
Control 4	319	10600	5183	670	214	4.0
Control 5	246	9100	5305	461	113	2.1
Control 6	218	5950	3403	860	187	5.2
Control 7	286	7300	4190	294	84	2.0
Control 8	187	7733	3952	536	100	2.5
Control 9	324	8205	4201	654	212	6.6
Control 10	232	8845	5316	507	118	2.8
Control 11	267	10120	5991	820	219	2.0
Control 12	288	7497	4506	579	167	3.6
Control 13	205	7250	4401	681	140	3.1
Control 14	254	12129	6174	864	219	3.4
Control 15	239	8329	4389	596	142	3.1
Mean (±SD)	267 (±65)	8334 (±1615)	4615 (±815)	634 (±158)	171 (±67)	3.7 (±1.6)
LMAN1 group
B26-1	210	1050	609	75	16	2.5
B26-2	130	789	633	62	13	2.6
B28	211	1150	447	128	17	2.8
A24	258	1850	1073	172	44	4.0
Mean (±SD)	202 (±53)	1210 (±453)	690 (±268)	109 (±51)	23 (±15)	3.0 (±0.7)
MCFD2 group
B27-1	193	570	335	54	10	3.0
B27-2	238	790	466	67	16	3.3
Zhang7-2	206	580	319	54	11	3.4
Mean (±SD)	212 (±23)	647 (±124)	373 (±81)	58 (±7)	13 (±3)	3.2 (±0.2)
Ratios
LMAN1/Wt.			0.15		0.13
MCFD2/Wt.			0.08		0.08

Plasma and platelet FV antigen levels were measured by ELISA. Plasma FV and platelet FV were normalized to the hematocrit and platelet counts, respectively, to determine the amount of FV of each pool in whole blood.

plts indicates platelets.