Table 1.
Distribution of age, onset of organ involvement and disease subsets
| Age (yrs) | Age at RP onset (yrs) | Age at skin involvement (yrs) | Age at organ involvement (yrs) | |
|---|---|---|---|---|
| Total | 55.7 ± 13.7 | 44.3 ± 15.6 | 47.9 ± 14.4 | 50.3 ± 14.2 |
| Family case history | 53.7 ± 13.0 | 41.5 ± 15.4 | 46.1 ± 14.0 | 47.9 ± 13.6 |
| Female | 56.0 ± 13.9 | 44.2 ± 15.8 | 48.1 ± 14.6 | 50.5 ± 14.5 |
| Male | 53.9 ± 12.4 | 45.1 ± 14.6 | 47.0 ± 13.4 | 49.1 ± 12.4 |
| Overlap-S. | 50.9 ± 13.5 | 40.5 ± 15.7 | 43.6 ± 15.5 | 45.0 ± 14.6 |
| Undiff. Scl. | 54.7 ± 12.5 | 46.8 ± 14.6 | 49.6 ± 12.5 | 50.9 ± 13.3 |
| Scl. sine Scl. | 54.1 ± 15.8 | 42.7 ± 14.9 | 48.1 ± 14.3 | 48.2 ± 16.0 |
| dcssc | 54.1 ± 14.1 | 44.5 ± 15.2 | 46.4 ± 14.3 | 48.6 ± 14.3 |
| lcSSc | 58.5 ± 12.7 | 44.7 ± 15.8 | 49.9 ± 14.0 | 52.2 ± 13.7 |
Values expressed as mean ± s.d. Overlap-S: Overlap syndrome; Undiff. Scl: Undifferentiated scleroderma; Scl. sine Scl.: sclerosis (scleroderma) sine scleroderma; dcSSc: diffuse cutaneous systemic sclerosis; lcSSc: limited cutaneous systemic sclerosis.