. Author manuscript; available in PMC: 2009 May 1.

Published in final edited form as: Mol Genet Metab. 2008 Feb 11;94(1):52–60. doi: 10.1016/j.ymgme.2007.12.008

Table 3.

Neurocognitive studies and results. All subjects were tested with a neurocognitive battery including Weschler Abbreviated scales of intelligence (WASI), Behavior Rating inventory of executive function (BRIEF), Comprehensive trails making test (CTMT) and the STROOP test.

	WASI			BRIEF A			CTMT		Stroop
	Full Scale	Verbal	Performance	BRI	MI	GEC	Composite	Percentile	Reaction Time
Subject 1 (III.1.)	114	110	114	37	38	36	46	35	628 ms
Subject 2 (III.3.)	83	88	81	64	78	74	20	<1	1279 ms
Subject 3 (II.2.)	107	106	107	63	64	65	42	3	875 ms
Subject 4 (Control)	126	119	126	36	40	37	68	96	705 ms

Key. WASI=Weschler abbreviated scales of intelligence; BRIEF=Behavior Rating Inventory of Executive Function; CTMT=comprehensive trail making test; STROOP=test of mental flexibility.