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. 2008 Aug 4;14:1429–1436.

Table 2. Polymorphic sequence variations identified in this study.

Gene Variation Allele frequency Reference Gene Variation Allele frequency Reference Gene Variation Allele frequency Reference
GUCY2D c.154G>T (A52S) 0.75 [23] RPGRIP1 c.287C>A (P96Q) 0.05 [26] CRX IVS3-67G>A 0.08
  c.741C>T (H247H) 0.15     c.450C>G (L150L) 0.05     IVS3-131A>T 0.03
  c.1371C>T (C457C) 0.15     c.574A>G (K192E) 0.3 [26]   c.460A>G (T154A) 0.03
  IVS5+143C>T 0.03     IVS6-14_16delAAT 0.28   RDH12 IVS2+60G>A 0.4
  IVS6+72C>T 0.03     IVS7+26T>C 0.65     IVS2-13insT 0.08
  c.2101C>T (P701S) 0.18 [24]   IVS9-65G>A 0.35     IVS2-58A>G 0.03
RPE65 c.-20G>A 0.03     IVS11-8C>T 0.03     IVS3-115G>C 1
  IVS3-46G>A 0.15     IVS13+148delG 0.03     c.482G>A (R161Q) 0.08 [28]
  IVS9+112T>C 0.25     c.1797G>A (P599P) 0.03     c.570C>T (S190S) 0.03
  c.1056G>A (E352E) 0.33     c.3097G>C (E1033Q) 0.43 [26] TULP1 IVS1+57T>C 0.03
  IVS12+20A>C 0.4     IVS21-148T>G 0.03     IVS1+58G>C 0.03
AIPL1 c.1-106C>A 0.3     IVS21-27T>A 0.03     IVS1+62_67delAGTGGG 0.03
  c.1-107G>A 0.03     IVS22+154A>G 0.1     IVS2+18G>A 0.08
  IVS1+36C>T 0.08     IVS23+17delT 0.03     IVS2+154A>G 0.73
  IVS1+45T>C 0.08   CRB1 IVS1-12A>T 0.83     IVS3+81G>C 0.53
  IVS1+105C>A 0.08     c.747C>T (D249D) 0.03     c.200C>G (T67R) 0.85 [29]
  IVS1+148G>A 0.03     IVS3-64A>G 0.03     IVS4-29C>T 0.03
  c.268G>C (D90H) 0.3 [25]   IVS3-35T>C 0.68     IVS5+26C>T 0.75
  IVS2-14G>A 0.03     IVS4+35C>T 0.1     IVS5+170T>C 0.7
  IVS2-10A>C 0.45     IVS4-53T>G 0.68     IVS7+108A>G 0.55
  c.300A>G (L100L) 0.53     c.1410A>G (L470L) 1     IVS7-63G>A 0.8
  IVS3-26T>C 0.1     c.2306G>A (R769H) 0.05 [27]   c.776T>C (I259T) 0.58 [30]
  IVS4+48G>A 0.5     IVS7-129C>A 0.03     c.783G>C (K261N) 0.83
  IVS4-33C>T 0.33     c.2796G>A (P932P) 0.03     IVS8+83G>A 0.03
  c.651A>G (P217P) 0.73     c.2809G>A (A937T) 0.03     IVS8-76T>C 0.13
  IVS5+18G>A 0.08     IVS8+87C>G 0.03     IVS8-17G>C 0.28
  IVS5+89C>T 0.33     IVS10+88insT 0.1     IVS13+90A>G 0.1
                  IVS13-87T>C 0.05

All polymorphic sequence variations in nine genes are presented here. Allele frequency was estimated in the patient group. Ten among thirteen missense variants were previously reported as polymorphic variants elsewhere. Three novel ones including c.2809G>A in CRB1, c.460A>G in CRX and c.783G>C in TULP1 were classified as polymorphic variants.