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. 2008 Sep 10;9:22. doi: 10.1186/1471-2091-9-22

Table 3.

Specific enzyme analysis of ADOA patient and control mitochondria

Mean specific enzyme activities
nmol/min/mg mitochondrial protein

Complex I Complex III Complex IV CSa
aOPA1+ (n = 6)
P2 82 1076 884 1410
P3 274 976 568 2074
P4 294 928 1005 1693
P6 86 1313 970 918
P7 52 1078 974 846
P8 122 845 828 1018
Mean ± SD 152 ± 105 1036 ± 162 872 ± 162 1327 ± 488
aOPA1- (n = 10)
Mean ± SD 190 ± 144 945 ± 174 810 ± 204 1154 ± 650
Control (n = 10)
Mean ± SD 170 ± 64 886 ± 179 893 ± 271 1304 ± 364

aAbbreviations used above are CS, citrate synthase, OPA1+, OPA1-positive patients, and OPA1-, OPA1-negative patients