Table 1. Patient characteristics.

Parameter	Value
Patients with PAH	10
Age, years	56.4 (31–79)
Disease duration, years	10.2 (2–24)
FVC/DLCO ratio	1.6 (1.37–2.13)
ANA (n)	10
SCL70 (n)	2
ACA (n)	2

Values are mean (range).

ACA, anticentromere antibodies; ANA, antinuclear antibodies; DLCO, CO diffusion; FVC, forced vital capacity; PAH, pulmonary arterial hypertension.