Table 3. Relapses/progressions in 16 stage 1 patients without MYCNA.
Case no. | Age (months) | Primary site | Histopathology | LDH | Ploidy | Site/time to relapse/progression | Therapy | Outcome |
---|---|---|---|---|---|---|---|---|
1 | 0 | A | — | E | — | Skin, 4 months | None | CR, 81 months |
2 | 1 | A | F | N | — | B, Skin, L, 3 months | None | CR, 74 months |
3 | 1 | Neck | F | — | An | Local, 3 months | CT | CR, 122 months |
4 | 1 | A | F | — | An | Local, 10 months | CT | CR, 87 months |
5 | 2 | A | F | N | — | L, 2 months | CT | CR, 62 months |
6 | 2 | A | F | N | An | B, Skin, L, 5 months | None | CR, 67 months |
7 | 5 | A | F | N | D | Local, B, 11 months | None | CR, 58 months |
8 | 7 | A | F | N | An | BM, 1 month | CT | CR, 117 months |
9 | 10 | T | F | N | An | Local, 3 months | None | CR, 112 months |
10 | 11 | A | F | N | D | Local, 48 months | CT, RT | CR, 92 months |
11 | 26 | T | F | — | An | Local, 23 months | CT, S | CR, 37 months |
12 | 26 | A | U | N | An | B, BM, 3 months | CT, S | CR, 127 months |
13 | 52 | A | — | E | D | BM, 11 months | None | CR, 70 months |
14 | 59 | A | — | N | — | Local, B, 10 months | CT | CR, 89 months |
15 | 71 | T | — | — | D | Local, BM, 5 months | CT | DOD, 24 months |
16 | 169 | A | — | — | — | Local, B, BM, 35 months | CT, RT | TD, 38 months |
A=abdomen; An=aneuploid; B=bone; BM=bone marrow; CR=complete remission; CT=chemotherapy; D=diploid; DOD=dead of disease; E=elevated; F=favourable; L=liver; N=normal; RT=radiotherapy; S=surgery; T=thorax; TD=toxic death; U=unfavourable.