Table 1.
Pheochromocytomas/paragangliomas | Carcinoids | |
---|---|---|
Epidemiology | 1–4/106 | 1–2/106 |
Localization | Adrenal and extra-adrenal (mainly torso) | Fore-, mid- and hindgut |
Genetics | Mostly sporadic; however an increasing number of patients (>20%) are currently found to have mutations in RET, VHL, NF-1, SDHx | Mostly sporadic; mutations in MEN1, bcl2 |
Products | Catecholamines | Serotonin |
Signs | Tachycardia, diaphoresis, hypertension (paroxysmal); pallor | Excess gastrointestinal motility |
Symptoms | Cephalalgia, Palpitations | Flushing |
Anatomical imaging | CT, MRI | CT, MRI |
Functional imaging | [18F]DA, [18F]DOPA, [123I]MIBG, SRS | [18F]DOPA, [11C]5-HTP, SRS |
Median survival | 50% | 67% |
Please see text for abbreviations