TABLE 1.
Characteristic | Number (N=2041) |
% | |
---|---|---|---|
Gender | Male | 952 | 47 |
Female | 1089 | 53 | |
Age at Diagnosis | Median 48 (16 – 93) |
||
Presentation Status | Primary Disease | 1665 | 82 |
Locally Recurrent | 376 | 18 | |
Site | Extremity | 937 | 46 |
Retroperitoneal/Intraabdominal | 328 | 16 | |
Trunk | 315 | 15 | |
Thoracic | 159 | 8 | |
Visceral¶ | 154 | 8 | |
Other† | 148 | 7 | |
Histology | Liposarcoma | 731 | 36 |
Desmoid/Fibromatosis¶¶ | 377 | 18 | |
Dermatofibrosarcoma Protuberans (DFSP) | 191 | 9 | |
Malignant Fibrous Histiocytoma | 181 | 9 | |
Leiomyosarcoma | 128 | 6 | |
Solitary Fibrous Tumor/Hemangiopericytoma | 113 | 5.5 | |
Fibrosarcoma | 91 | 4.5 | |
Chondrosarcoma†† | 34 | 2 | |
Endometrial Stromal Sarcoma | 34 | 2 | |
Other¶¶¶ | 163 | 8 | |
Primary Tumor Size | ≤ 5 cm | 723 | 35 |
5-10 cm | 539 | 26 | |
> 10 cm | 678 | 33 | |
Unknown | 101 | 5 | |
Depth | Deep | 1576 | 77 |
Superficial | 448 | 22 | |
Margin Status | R0 | 1391 | 68 |
R1 | 463 | 23 | |
R2 | 105 | 5 | |
Unknown | 82 | 4 | |
Radiotherapy | Primary Tumor | 292 | 14 |
Recurrent Disease | 196 | 10 | |
Chemotherapy | Primary Tumor | 65 | 3 |
Recurrent Disease | 156 | 8 | |
Disease Recurrence | Local | 667 | 33 |
Distant | 171 | 8 | |
Both | 120 | 6 | |
Status at Last Follow- Up |
No evidence of disease | 1486 | 73 |
Alive with disease | 135 | 7 | |
Dead of other causes | 239 | 12 | |
Dead of disease | 181 | 9 |
Because of rounding, not all percentages sum to 100.
Includes gynecologic 65/154 (42%), gastrointestinal 61/154 (40%), and genitourinary 28/154 (18%).
Includes head and neck 121/2041 (6%) and skin 27/2041 (1%).
Analyses performed excluding patients with desmoids/fibromatosis obtained similar results.
Includes extraskeletal myxoid chondrosarcoma 33/34 (97%), mesenchymal chondrosarcoma 1/34 (3%).
Comprises 19 histologic subtypes including cystosarcoma phyllodes, sarcoma NOS (not otherwise specified), malignant peripheral nerve sheath tumor, angiosarcoma, follicular dendritic cell tumor, synovial sarcoma, and malignant mesenchymoma among others.