Table 1.

Comparison of prevalence and frequency of major criteria in NBCCS patients among four studies.

	Evans et al. [5] United Kingdom, 1993	Shanley et al. [12] Australia, 1994	Kimonis et al. [6] United States, 1997	Lo Muzio et al. [11] Italy, 1999	Ahn SG et al. [14] Korea, 2004	Pruvost-Balland et al. [15] France, 2006
Patients	84	118	105	37	33	22
Prevalence	1/56,000	1/164,000	NR	1/256,000	1/13,939,393	NR
Major criteria % or (% African-Americans)
BCCs	47	76	80 (38)	30	15.2	100
Age > 20 y	73	85	91	17	-	-
Age > 40 y	90	95	97	75	-	-
Jaw cyst	66	75	74	92	90.9	62
Palm/plant pits	71	80	87	35	66.7	45
Calcification of falx cerebri	NR	92	65	70	21.2	66

NBCCS = Nevoid basal cell carcinoma syndrome; NR-Non reported