Table 1.

Baseline Clinical Characteristics of 5 LQT3 Study Patients with ΔKPQ Mutation

	Patient No.
	1	2	3	4	5	Mean±sd
Age, y	55	35	47	24	39	40±12
Sex	M	M	F	M	M
Height, cm	169	180	173	163	188	175±10
Weight, kg	103	75	61	65	79	77±16
Syncopal history	N	N	N	Y	Y
Beta-blocker	Y	Y	N	Y	Y
Atrial pacemaker	N	N	N	N	Y
ICD	N	Y	N	Y	N
ECG
Rhythm	sinus	sinus	sinus	atrial paced	atrial paced
PR, ms	230	200	200	200	240	214±19
QRS, ms	110	80	90	80	80	88±13
RR, ms	1470	1400	900	1000	1000	1154±261
QT, ms	720	700	480	550	580	606±107
QTc, Fridericia, ms	630	630	500	550	580	578±55
QTpeak, ms	590	570	400	460	460	496±81
Tpeak-Tend, ms	130	130	80	90	120	110±23
Tduration, ms	250	240	170	170	210	208±38
Tamp, mv	0.3	0.2	0.2	0.3	0.3	0.28±0.04