Figure 2.

Cutaneous findings in the proband (A–E) and her brother (F,G) with PXE-like phenotype. Note the yellowish papules and plaques in the lateral and posterior neck (A,C), which on close examination demonstrate characteristic features of PXE (E). Also note the loose and sagging skin primarily in the groin (B) and axillary (D) areas. The loose skin was also noted in the proband’s brother in the lateral neck (F) and axillary areas (G). (A, C) the lower border of the plaque is demarcated by arrows in C.