Table 6.
Chronic treatment of UCD patients: N (%)
Disorder | Phenylbutyrate | Arginine | Benzoate | Citrulline | Protein restriction |
---|---|---|---|---|---|
AL | 6 (21) | 23 (79) | 2 (7) | 0 (0) | 22 (76) |
AS | 13 (50) | 15 (58) | 1 (4) | 0 (0) | 17 (65) |
OTC | 36 (37) | 2 (2) | 1 (1) | 44 (45) | 58 (57) |
Others | 4 (25) | 0 (0) | 3 (19) | 3 (19) | 10 (63) |
UCD likely | 7 (64) | 1 (9) | 2 (18) | 9 (82) | 8 (73) |
Total | 66 (37) | 41 (23) | 9 (5) | 56 (31) | 115 (63) |