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. Author manuscript; available in PMC: 2009 Aug 1.
Published in final edited form as: Mol Genet Metab. 2008 Jun 17;94(4):397–402. doi: 10.1016/j.ymgme.2008.05.004

Table 6.

Chronic treatment of UCD patients: N (%)

Disorder Phenylbutyrate Arginine Benzoate Citrulline Protein restriction
AL 6 (21) 23 (79) 2 (7) 0 (0) 22 (76)
AS 13 (50) 15 (58) 1 (4) 0 (0) 17 (65)
OTC 36 (37) 2 (2) 1 (1) 44 (45) 58 (57)
Others 4 (25) 0 (0) 3 (19) 3 (19) 10 (63)
UCD likely 7 (64) 1 (9) 2 (18) 9 (82) 8 (73)
Total 66 (37) 41 (23) 9 (5) 56 (31) 115 (63)