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. 2006 Aug;3(6):499–501. doi: 10.1513/pats.200603-069MS

TABLE 1.

CORRELATION BETWEEN THE RATE OF POLYMERIZATION OF MUTANTS OF NEUROSERPIN, THE NUMBER OF INCLUSIONS, AND THE SEVERITY OF THE ASSOCIATED DEMENTIA

Mutation Rate of Polymerization Inclusions Age of Onset (yr) Clinical Features
Ser49Pro + + 45–63 Dementia, seizures
Ser52Arg ++ ++ 20–40 Dementia, myoclonus
His338Arg +++ +++ 15 Progressive myoclonus epilepsy
Gly392Glu ++++ ++++ 13 Progressive myoclonus epilepsy, chorea

Reproduced by permission from Reference 16.