Figure 5. Potential mechanism for enhancement of TGF-β signaling in the presence of non-functional receptors.
Ligand-induced receptor signaling complexes that are unable to transmit signals because of mutations within the receptor kinase domain (TGF-βRII/TGF-βRI/both), may still function by seeding active signaling platforms that localize other signaling components capable of inducing downstream signaling events that contribute to aneurysm development.