Table 1.

Liver Gb₃ concentrations pre- and post-α-gal A administration

Patient	Predose Gb3, nmol/mg	Postdose Gb3, nmol/mg	Gb3 change, nmol/mg	Percent change from baseline
0001	25.05	15.94	−9.11	−36
0002	5.29	4.54	−0.75	−14
0003	2.43	5.82	+3.39	+140
0004	6.95	5.49	−1.46	−21
0005	7.77	5.09	−2.68	−34
0006	4.25	3.07	−1.18	−28
0007	6.44	3.36	−3.08	−48
0008	0.33	0.14	−0.19	-48
0009	7.88	2.3	−5.58	−71
0010	12.18	8.89	−3.29	−27
Mean	7.86	5.46	−2.40	−31