Table 3.

Characteristics of renal involvement at kidney biopsy and last follow-up in 13 adult patients with CF^a

Patient	Age (yr)b	SCr (mmol/L)/GFR (ml/min per 1.73 m2)	Serum Albumin (g/L)	Proteinuria	Hematuria	Hypertension	Renal Pathology	Treatment	Outcome
1	24	107/78	40	0.60 g/L	−	+	Exsudative GN	–	Complete remission
2	20	105/83	44	1.20 g/d	−	+	FSGS calcium oxalate crystals	ARB	NS, CRI, ARF after PT
3	27	64/138	34	0.45 g/L	−	+	KW	ACEI	SCr 88 μmol/L, Pu 1.8 g/d
4	31	71/119	27	1.50 g/d	−	+	KW	ACEI	SCr 156 μmol/L, NS
5	49	66/88	28	9.50 g/d	−	−	AA amyloidosis	ACEI	ESRDc
6	43	53/116	21	1.20 g/L	−	−	MCD, CTIN	–	Spontaneous remission, PT, SCr 150 mmol/L
7	23	74/121	30	0.12 g/L	+++	−	IgAN	ACEI	PTc
8	33	69/122	21	10.00 g/d	−	−	MN	ACEI/ARB	PT
9	23	140/58	26	0.15 g/L	−	−	AA amyloidosis	ACEI	PKT, SCr 60 μmol/L, Pu 0.5 g/L
10	26	63/142	36	>3.00 g/L	−	−	FSGS	ACEI	c
11	32	97/83	27	2.20 g/L	+	−	KW		LT and PT
12	46	55/110	32	0.60 g/d	−	−	CTIN	–	PT, SCr 90 mmol/L
13	37	144/51	23	1.00 g/d	−	−	AA amyloidosis	–	CRF, SCr 145 mmol/L

^aACEI, angiotensin-converting enzyme inhibitor; ARB angiotensin II receptor blocker; ARF, acute renal failure; CRI, chronic renal insufficiency; CRF, chronic renal failure; CTIN, chronic tubulointerstitial nephropathy; GN, glomerulonephritis; IgAN, IgA nephropathy; KW, Kimmelstiel-Wilson glomerulosclerosis; LT, liver transplantation; MCD, minimal-change disease; MN, membranous nephropathy; NS, nephrotic syndrome; PKT, pulmonary and kidney transplantation; PT, pulmonary transplantation; Pu, proteinuria; SCr, serum creatinine.

^bAge at the time of kidney biopsy.

^cDeath.