FIG. 2.

Plasma glucose and β-hydroxybutyrate responses to fasting in child 2. Mean plasma glucose was 64 ± 1 mg/dl. β-Hydroxybutyrate values increased from 0.1 to 1.8 mmol/l, whereas fasting plasma glucose levels decreased. At the end of the fast, plasma C-peptide was suppressed (0.16 nmol/l, normal 0.26–1.32 nmol/l). Glucose response to glucagon stimulation was 36 mg/dl. Reference normals when fasting blood glucose <50 mg/dl: β-hydroxybutyrate >2.5 mmol/l, and glycemic response to glucagon >30 mg/dl. △, plasma glucose (SureStep bedside meter); ▲, β-hydroxybutyrate (Precision Xtra bedside meter).