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. Author manuscript; available in PMC: 2009 Jul 1.
Published in final edited form as: J Inherit Metab Dis. 2009 Jan 28;32(3):343–352. doi: 10.1007/s10545-009-1034-y

Table 5.

Ataxia/motor problems in adolescent and adult patients (N= 35)

n %
Decreased balance 18 51%
Uncoordinated movements 11 31%
Wide based gait 11 31%
Uncoordinated walking 10 29%
Hand tremors 7 20%
Excessive movements 6 17%