Table 1.
Demographics, diagnoses, types of portosystemic shunt and outcomes in children with intrinsic liver disease
| Patient | Sex | Diagnosis | Age at shunt, years | Type of shunt | Follow-up, years | Outcome |
|---|---|---|---|---|---|---|
| 1 | M | Biliary atresia | 2.8 | DSRS | 1.2 | Patent shunt |
| 2 | M | Biliary atresia | 3.9 | DSRS | 0.2 | Patent shunt |
| 3 | F | Biliary atresia | 5.5 | DSRS | 0.2 | Patent shunt |
| 4 | M | Biliary atresia | 8.8 | Mesocaval | 14.1 | Liver transplant |
| 5 | M | Congenital hepatic fibrosis | 16.7 | DSRS | 11.7 | Liver transplant |
| 6 | M | Congenital hepatic fibrosis | 6.4 | DSRS | 1.1 | Patent shunt |
| 7 | M | Cryptogenic cirrhosis | 18.0 | DSRS | 5.8 | Patent shunt |
| 8 | F | Cryptogenic cirrhosis | 22.1 | DSRS | 3.6 | Patent shunt |
| 9 | F | Autoimmune hepatitis | 18.6 | DSRS | 6.1 | Death (non-adherence) |
| 10 | M | Wilson's disease | 10.7 | DSRS | 0.3 | Patent shunt |
| 11 | F | Cystic fibrosis | 12.9 | DSRS | 4.7 | Patent shunt |
| 12 | M | Lymphoma | 17.9 | Proximal splenorenal | 0.2 | Death secondary to lymphoma |
M, male; F, female; DSRS, distal splenorenal shunt