Table I. Cutaneous Findings in NF1.
Common | Uncommon or Reported Associations |
---|---|
Café-au-lait macules* | Juvenile xanthogranuloma (JXG) |
Axillary/Inguinal Freckling (Crowe's sign)* | Glomus tumor |
Neurofibromas (dermal, plexiform)* | Melanoma |
Increased base pigmentation | Blue-red macules |
Pseudoatrophic macules | |
Nevus anemicus |
Diagnostic criterion for NF1