Table 2.
Autoantigens | ||
Mitochondrial antigens | E2 subunits of 2-OADC | PDC-E2 |
OGDC-E2 | ||
BCOADC-E2 | ||
Pyruvate dehydrogenase | E3BP | |
complex | PDC E1α | |
Nuclear antigens | Nuclear pore complex | gp210 |
nucleoporin 62 | ||
Multiple nuclear dots | Sp100 | |
PML | ||
Anticentromere |
2-OADC: 2-oxo-acid dehydrogenase complex; PDC: Pyruvate dehydrogenase complex; OGDC: Oxoglutarate dehydrogenase complex; BCOADC: Branched chain 2-oxo-acid dehydrogenase complex; E3BP: Dihydrolipoamide dehydrogenase (E3)-binding protein.