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. 2008 Jun 7;14(21):3328–3337. doi: 10.3748/wjg.14.3328

Table 2.

Mitochondrial and nuclear autoantigens in PBC

Autoantigens
Mitochondrial antigens E2 subunits of 2-OADC PDC-E2
OGDC-E2
BCOADC-E2
Pyruvate dehydrogenase E3BP
complex PDC E1α
Nuclear antigens Nuclear pore complex gp210
nucleoporin 62
Multiple nuclear dots Sp100
PML
Anticentromere

2-OADC: 2-oxo-acid dehydrogenase complex; PDC: Pyruvate dehydrogenase complex; OGDC: Oxoglutarate dehydrogenase complex; BCOADC: Branched chain 2-oxo-acid dehydrogenase complex; E3BP: Dihydrolipoamide dehydrogenase (E3)-binding protein.