Table 1.
Neuromuscular disease patient demographics.
| Patient number |
Age (y) |
Gender | Diagnosis | MRC score of tibialis anterior studied with EIM |
Approximate mean MMT score for all muscles examined |
Disease duration (y) |
Weakest muscles |
|---|---|---|---|---|---|---|---|
| 1 | 40 | M | ALS | 4 | 3+ | 4 | Bilateral biceps |
| 2 | 54 | F | ALS | 0 | 4 | 2 | Bilateral tibialis anterior |
| 3 | 73 | M | ALS | 4 | 4 | 3 | Bilateral tibialis anterior |
| 4 | 75 | F | ALS | 0 | 4+ | 4 | Ipsilateral tibialis anterior |
| 5 | 76 | M | ALS | 3 | 4− | 3 | Ipsilateral tibialis anterior |
| 6 | 79 | F | ALS | 2 | 4 | 2 | Bilateral tibialis anterior |
| 7 | 32 | M | Dysferlin myopathy | 2 | 3 | 9 | Bilateral tibialis anterior |
| 8 | 44 | M | HIV-associated IBM | 5 | 4+ | 12 | Ipsilateral quadriceps |
| 9 | 44 | M | FSHD | 4+ | 4 | 28 | Bilateral biceps |
| 10 | 58 | M | s-IBM | 5− | 4+ | 4 | Bilateral triceps |
| 11 | 70 | F | s-IBM | 5− | 4+ | 1 | Bilateral finger flexors |
| 12 | 83 | F | s-IBM | 4− | 4− | 26 | Ipsilateral quadriceps |
ALS, amyotrophic lateral sclerosis; MRC, Medical Research Council; MMT,;HIV, human immunodeficiency virus; s-IBM, sporadic inclusion-body myositis; FSHD, fascioscapulohumeral muscular dystrophy.