Table 1.
Disorder | Years of Age/Sex |
Radiation Treatment |
Outcome | Reference |
---|---|---|---|---|
A-T | 10.5/M | 30 Gy | Died, 8 months | (7) |
A-T | 9/M | 27.5 Gy (mediastinal tumor) 27.5 Gy (supraclavicular area) |
Died, 3 months | (61) |
A-T | 3.9/M | 3 Gy | Died, < 1 month | (58) |
A-T | 7/M | 30 Gy | Died, 3 weeks | (62) |
A-T | 3.8/F | 30 Gy | Died, 9 months | (63) |
A-T | 9/M | 16 Gy | Severe mucosal ulceration |
(64) |
A-T | 4.5/M | 18 Gy | Leukoencephalopathy | (65) |
A-T | 7/M | 24 Gy (brain) 12 Gy (spine) |
Somnolescence syndrome |
(66) |
A-T | 9/F | 9 Gy | Died, 10 months | (67) |
A-T | 15.2/M | 15.5 Gy | Died,1 month | (59) |
A-T | 3.9/M | 3 Gy | Died, 3 months | (59) |
A-T | 1.5/M | 18 Gy (brain) 3 Gy (chest) |
No excessive toxicity | (68) |
A-T | 2.5/M | 24 Gy (brain) 6 Gy (spine) |
Leukoencephalopathy, 10 months |
(68) |
NBS | 5/M | 36 Gy | Died, 18 months | (69) |
NBS | 3/M | 23.4 Gy (craniospinal) 55.8 Gy (posterior fossa) |
Interstitial pneumonitis, Died, 3 months |
(23) |
FA | 26/F | NS | Died, 4 months | (70) |
FA | 17/F | 68 Gy | Died, 3 months | (71) |
FA | 22/M | NS | Alive, 10 months post | (72) |
FA | 26/M | 70 Gy | Died during RT | (73) |
FA | 27/F | 42.5 Gy | Severe moist skin reaction, Died, 3 months |
(74) |
FA | 23/F | NS | Died, 4 years | (75) |
FA | 20/F | NS | Died, 2 months | (76) |
FA | 14/M | 80 Gy | Died, 6 months | (77) |
FA | 25,29/F | 72 Gy | Died, 6 months | (78) |
FA | 12/M | NS | Died, 4 months | (79) |
FA | 29/F | 32.5 Gy | Died, 12 months | (80) |
FA | 32/F | 3.2 Gy | Died, 9 months | (81) |
FA | 18/F | NS | Died, 3 months | (82) |
FA | 32/F | 34 Gy | Ulcerating oropharyngeal mucositis, Alive, 3 months |
(83) |
FA | 14/F | 21.6 Gy | Dead | (84) |
FA | 29/F | NS | Died, 9 months | (32) |
FA | 24/M | 67 Gy, 55.8 Gy, 25.2 Gy |
Died, 3 months | (37) |
FA | 32/M | 8 Gy | Died, < 1 week | (37) |
FA | 25/F | 9 Gy | Died, 1 week | (33) |
Ligase IV |
14/M | 18 Gy | Died, 8 months | (44) |
Bloom | 33/F | 60 Gy | severe, acute radiation toxicity |
(85) |