Table 1.
Disease association | Number (%) |
---|---|
Pulmonary | |
Asthma | 108 (68) |
Kartagener | 4 (3) |
Foreign body aspiration | 6 (4) |
Immotile cilia syndrome site | 17 (11) |
Lipid pneumonia | 7 (5) |
Interstitial pneumonia | 2 (1.3) |
ABPA | 2 (1.3) |
Tuberculosis | 2 (1.3) |
RML syndrome | 1 (0.6) |
TEF repair | 4 (3) |
Bronchogenic cyst | 7 (5) |
Lung collapse | 3 (2) |
Prematurity | 3 (2) |
Cardiac diseases: | |
Dextrocardia | 4 (3) |
Congestive heart failure | 1 (0.6) |
Ventricular septal defect | 2 (1.3) |
Atrial septal defect | 1 (0.6) |
Pulmonary hypertension | 1 (0.6) |
Mitrale valve prolapse | 1 (0.6) |
Skeletal: | |
Pectus excavatum | 2 (1.3) |
Scoliosis | 4 (3) |
Absent ribs | 3 (2) |
Marfan's syndrome | 1 (0.6) |
Immunodefficiency | |
Hypogammaglobulinemia | 3 (2) |
SCIDS | 3 (2) |
Human immunodeficiency virus | 1 (0.6) |
Hyper IgE | 1 (0.6) |
IgG subclass defficiency | 6 (4) |
Hyper IgM | 2 (1.3) |
Whiscott Aldrich syndrome | 1 (0.6) |
Poor antibodies response | 4 (3) |
Common variable- | 3 (2) |
Hypogammaglobulinemia | 3 (2) |
T-cell deficiency | 1 (0.6) |
Barre lymphocyte syndrome | |
Central nervous system disease: | |
Cerebral palsy/ seizure disorder | 4 (3) |
Apnea | 1 (0.6) |
Craniosynostosis | 1 (0.6) |
Cutis laxa/ developmental delay | 1 (0.6) |
Down syndrome/seizure | 2 (1.3) |
Fatty acid oxidation defect | 1 (0.6) |
Other disease associations: | |
Neuroblastoma | 1 (0.6) |
Antithrombin III defficiency | 2 (1.3) |
Corrosive ingestion | 2 (1.3) |
Liver cirrhosis | 1 (0.6) |
Ethmoid mucocele | 1 (0.6) |
Bulllous skin lesion/septicemia | 1 (0.6) |
FBA - Foreign body aspiration, ABPA - Allergic bronchopulmonary aspergillosis, TB - Tuberculosis, RML - Right middle lobe, TEF - Tracheoesophageal fistula, SCIDS - Severe combined Immunodefficiency