Table 1.
Activity (nmol/ml/h) |
-Fold increase |
|||
---|---|---|---|---|
Wild-type | UCE(−/−) | UCE(−/−) | GNPTAB(−/−)a | |
β-Hexosaminidase | 272 ± 71 | 624 ± 121 | 2.3× | 6.7× |
α-Mannosidase | 978 ± 153 | 3045 ± 384 | 3.1× | |
β-Glucuronidase | 11 ± 5 | 59 ± 18 | 5.4× | 11.2× |
β-Mannosidase | 171 ± 31 | 293 ± 50 | 1.7× | 9.4× |
α-Galactosidase | 24 ± 6 | 45 ± 9 | 1.9× | |
β-Galactosidase | 23 ± 9 | 37 ± 8 | 1.6× | 13.9× |
β-Glucocerebrosidase | 49 ± 10 | 53 ± 11 | 1.1× |
a Data were collected from Gelfman et al. (2007).