Table 2.
Activity (nmol/ml/h) |
||||
---|---|---|---|---|
Wild-type brain (n = 4) | UCE −/− brain (n = 6) | Wild-type liver (n = 4) | UCE −/− liver (n = 4) | |
β-Hexosaminidase | 28.0 ±7.3 | 28.1 ±6.5 | 15.7 ± 5.7 | 22.1 ±4.9 |
β-Glucuronidase | 6.0 ± 1.3 | 5.9 ± 1.1 | 34.1 ± 12.7 | 40.5 ± 26.1 |
β-Mannosidase | 4.6 ± 1.6 | 5.7 ± 4.9 | 14.9 ± 8.1 | 10.5 ± 7.2 |
β-Galactosidase | 9.4 ± 3.3 | 12.1 ± 3.4 | 20.1 ± 7.9 | 26.9 ± 10.0 |