Table 2.
Penicillamine initiation in 11 children with cystinuria
| Patient | Sex | Age at initiation (y) | Toxicity | % decrease, [cystine]ur* |
|---|---|---|---|---|
| 1 | F | 6.9 | None | 79% |
| 2 | M | 2.8 | None | 81% |
| 3 | M | 1.2 | None | 54% |
| 4 | F | 11.8 | None | 58% |
| 5 | M | 1.5 | None | 58% |
| 6 | F | 2 | None | N/A1 |
| 7 | F | 17 | None | 38% |
| 8 | M | 12.5 | None | 36% |
| 9 | M | 4.3 | None | 51% |
| 10 | M | 7.3 | None | 5% |
| 11 | M | 12 | None | 34% |
*
% decrease, [cystine]ur = decrease in urinary cystine concentration between pretreatment specimen and first specimen on maintenance dose
1
No pre-treatment specimen available in our records.