TABLE 1.

Literature summary of optic nerve hemangioblastomas in patients with VHL disease

Authors & Year	Age (yrs), Sex	Symptoms	Lesion Side	Resection Performed	Tumor Origin	Visual Outcome
Stefani & Rothemund, 1974	20, M	total atrophy of rt optic nerve before death	rt	no	intraneural	not applicable
In et al., 1982	23, F	blindness, pulsating exophthalmos & absent direct-light reflex	lt	yes	intraneural	unchanged
Nerad et al., 1988	24, F	blindness, proptosis, papilledema, decreased sensation in V1	lt	yes	intraneural	unchanged
Ginzburg et al., 1992	44, M	bilat visual loss & optic disc pallor	bilat	yes	intraneural	unchanged
Rubio et al., 1994	43, F	absence of rt pupillary light reflex & absence of rt visual evoked response	rt	yes	intraneural	not reported
Kerr et al., 1995	40, F	visual acuity 14/224 in rt eye w/afferent defect	rt	yes	intraneural	unchanged
Raila et al., 1997	30, F	asymptomatic	lt	yes	peripheral	unchanged
Kouri et al., 2000	15, F	asymptomatic	lt	yes	peripheral	unchanged
present case	62, M	loss of color vision, vision for finger countting only in lt eye, & afferent defect	lt	yes	intraneural	improved