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. Author manuscript; available in PMC: 2009 Nov 8.
Published in final edited form as: Mol Genet Metab. 2008 Jun 5;94(4):448–455. doi: 10.1016/j.ymgme.2008.04.009

Figure 4.

Figure 4

Enzyme activity analysis of heart and quadriceps from GAA knockout mice administered CHO-GAA, tgGAA and HP-GAA for 4 weekly doses of 20, 60 and 100 mg/kg (mean ± SD). * indicates p<0.05 as compared to tgGAA and CHO-GAA; # indicates p<0.05 as compared to tgGAA and HP-GAA.