Table I.

Demographics

	Age of onset	Gender	Age at initial evaluation	Age (yrs) at most recent evaluation	Disease variant		Clinical outcome
					At diagnosis	At follow up
1	6m	F	3y	24	UP	UP	Major regression
2	3m	M	11m	21	UP	Resolved	Complete regression
3	6m	M	3y	23*	UP	Resolved	Complete regression
4	3m	F	3y	19	UP	UP	Major regression
5	2y	F	8y	26	UP	UP	Major regression
6	2y	M	5y	NF	UP	Unknown	Unknown
7	1m	M	2y	23*	UP	Resolved	Complete regression
8	4d	M	1y	21	UP	Resolved	Complete regression
9	3m	M	3m	21	DCM	Resolved	Complete regression
10	1y	M	3y	17	UP	Resolved	Complete regression
11	birth	M	5m	18	DCM	DCM	Partial regression
12	6w	M	4y	24*	UP	Resolved	Complete regression
13	2m	M	6m	20	UP	Resolved	Complete regression
14	birth	M	6m	20	UP	UP/ISM	Partial regression†
15	3m	M	3y	18	UP	Resolved	Complete regression
16	4m	M	7m	NF	UP	Unknown	Unknown
17	birth	M	3y	19	UP	Resolved	Complete regression

d-days, w-weeks, m-months, y-years; UP-Urticaria Pigmentosa, NF-no follow up, DCM-Diffuse Cutaneous Mastocytosis, and ISM-Indolent Systemic Mastocytosis

^*Contacted by phone only

^†Patient’s initial marrow re-read as diagnostic of indolent systemic mastocytosis