Table 3. Guidelines for who test for FXTAS.

Cerebellar ataxia	≥ age 50 & Unknown cause
Action tremor	Presence of cerebellar ataxia, parkinsonism or dementia & ≥ age 50 & Unknown cause
Dementia	Presence of cerebellar ataxia, parkinsonism or action tremor & ≥ age 50 & Unknown cause
Some FXTAS signs	Middle cerebellar peduncle sign or Patient or family history of premature ovarian insufficiency or Family history of FMR1 related disease
Multiple system atrophy, cerebellar subtype*

^*Especially if has action tremor or longer than expected disease duration