Table 1. Creutzfeldt-Jakob disease death rates and deaths, United States, 1979–2006.^* .

Characteristics	Death Rate (95% CI) †	Risk Ratio (95% CI) †	Number of Deaths (%)
Age group
<55 years	0.14 (0.13–0.15)	reference	781 (11.3)
≥55 years ‡	3.97 (3.87–4.07)	29.1 (27.0–31.4)	6136 (88.7)
Sex
Female	0.92 (0.89–0.95)	reference	3635 (52.6)
Male ‡	1.05 (1.01–1.09)	1.2 (1.2–1.3)	3282 (47.4)
Race
Black	0.40 (0.35–0.45)	reference	254 (3.7)
White ‡	1.04 (1.01–1.07)	2.7 (2.4–3.0)	6541 (94.6)
Other ‡	0.61 (0.50–0.73)	1.5 (1.2–1.9)	121 (1.7)
Region
South	0.84 (0.81–0.88)	reference	2103 (30.4)
Northeast ‡	1.08 (1.03–1.13)	1.2 (1.2–1.3)	1656 (24.0)
Midwest ‡	1.04 (0.99–1.09)	1.2 (1.1–1.2)	1793 (25.9)
West ‡	0.98 (0.93–1.04)	1.2 (1.1–1.2)	1363 (19.7)
Total	0.97 (0.95–0.99)		6917

^*Deaths obtained from the multiple cause-of-death data for 1979–1998 are based on ICD-9 codes and those beginning in 1999 are based on ICD-10 codes with available computerized literal death certificate data. Death information was also obtained from other surveillance mechanisms. One death is missing both race and region; and one death is missing region.

^†Death rates expressed per 1,000,000 persons in corresponding group. Death rates and risk ratios are age-adjusted for total, sex, race, and region. The 95% confidence intervals (CIs) are given.

^‡p<0.001 for comparison of death rate to that of the referent group.