Table 1.

Features of fetuses/infants born to anti Ro/La-negative mothers.

Patient	Sex	Year of Birth	GA CHB	Lower Fetal HR	GA at Delivery	HR at Birth	Apgar Score	Fetal Heart Failure	Age at Permanent Pacing	Features of Block	Outcome (2007)
1	M	2005	22	35	30	27	7–8	Ascites, LV dilatation	1 day	Stable 3rd degree	Died (at 5 mo from respiratory distress complicated by sepsis)
2	F	1996	32	30	36	58	8–9	No	1 day	Stable 3rd degree Dexamethasone 84 mg in utero pending autoantibody finding	Alive (congenital sensorineural deafness)
3	F	2005	19	45	37	40	8–8	Hydrops, LV dilatation	20 days	2nd degree, progressed to 3rd degree in utero and then stable. Betamethasone 102 mg in utero pending autoantibody finding	Died (suddenly at 2 mo despite pacing)
4	F	1999	At birth	80	41	100	8–10	No	1 yr	Stable 2nd degree	Alive
5	M	2001	29	80	34	70	7–9	No	No pacing	Stable 2nd degree	Alive
6	F	2005	At birth	80	34	75	7–8	No	20 days	2nd degree at birth; 3rd degree at 3 days	Alive
7	M	2001	At birth	96	41	96	9–10	No	4 mo	Extrasystoles at 29 and 30 wks; 2nd degree AV block at birth, 3rd degree at 3 mo	Alive
8	F	1996	29	40	35	60	5–7	No	No pacing	2nd degree alternating with 3rd degree in utero. Betamethasone 24 mg to enhance fetal lung maturity. 3rd degree at birth, reverted to NSR 30 min after birth but worsened to 2nd degree block the next day	Died (at 15 days from respiratory distress, pulmonary hypertension, and cardiac failure)
9	M	2005	29	80	34	110	9–9	No	No pacing	28 wks fetus in NSR; at 29 wks complete AV block was repeatedly found in 2 referral centers, over 3 days; betamethasone 12 mg was given to induce lung maturity; NSR the day after; 2 days later 3rd degree AV block recurred, and betamethasone was restarted, pending autoantibody finding; after 2 days NSR again, stable till delivery, at 34 wks; mother continued high-dose betamethasone (4 mg daily), from 29 to 34 wks	Alive (NSR at 2 yrs of age)

GA CHB: gestational age at detection of CHB weeks; HR: heart rate; AV: atrioventricular; LV: left ventricle; NSR: normal sinus rhythm.