Table 1.
Characteristics | Study sample (n=37) n (%) |
---|---|
Age (yr), mean (SD) | 44.62 (16.57) |
Sex (M/F) | 7/30 (18.9/81.1) |
Smoking | |
Non smokers | 31 (83.8) |
Ex-smokers | 6 (16.2) |
Chest symptoms | |
Cough | 34 (91.9) |
Grade 1 dyspnea | 1 (2.7) |
Grade 2 dyspnea | 1 (2.7) |
Grade 3 dyspnea | 25 (67.6) |
Grade 4 dyspnea | 10 (27) |
Corpulmonale | 25 (67.6) |
Central cynosis | 33 (89.2) |
Clinical signs of PH | 10 (27) |
Electrocardiogram findings | |
Normal | 17 (45.9) |
P-pulmonale | 17 (45.9) |
Rt ventricular strain | 3 (8.1) |
Pulmonary function tests, mean (SD) | |
FEV1, L | 1.11 (0.4) |
FEV1, % predicted | 49.11 (15.44) |
FVC, L | 1.46 (0.55) |
FVC, % predicted | 53.11 (18.42) |
FEV1/FVC | 91.59 (16.34) |
TLC, L | 3.24 (1.15) |
TLC, % predicted | 72 (22.08) |
DLCO, mL/mm Hg/min | 4.06 (2.07) |
DLCO, % predicted | 57.38 (31.28) |
Room air resting arterial blood gases, mean (SD) | |
O2 saturation | 85.88 (9.82) |
O2 tension | 55.07 (17.26) |
CO2 tension | 39.15 (7.8) |
Formula-predicted MPAP, mean (SD) | 34.59 (21.35) |
Echo measured RVSP, mm Hg, mean (SD) | 43.44 (17.84) |
Data are presented as mean (SD) or %. Patients characteristics were available in all of studied 37 patients; PH = pulmonary hypertension, FEV1 = forced expiratory volume in first second, FVC = forced vital capacity, TLC = total lung capacity, DLCO = diffusing capacity of the lung for carbon monoxide, RVSP = right ventricular systolic pressure as measured by trans thoracic echocardiography,