Table 2.
Clinical Description of Individuals with Hereditary Dysphasic Disinhibition Dementia (HDDD2) Kindred
Characteristics | HDDD (n = 26) |
---|---|
Sex, F/M | 13/13 |
Mean onset of disease (range), yr | 63.5 (52–77) |
Mean duration of disease (range), yr | 7.2 (6–11) |
Mean age at death (range), yr | 70.2 (59–86) |
HDDD = hereditary dysphasic disinhibition dementia.