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. Author manuscript; available in PMC: 2010 Jan 7.
Published in final edited form as: Ann Neurol. 2006 Sep;60(3):314–322. doi: 10.1002/ana.20963

Table 2.

Clinical Description of Individuals with Hereditary Dysphasic Disinhibition Dementia (HDDD2) Kindred

Characteristics HDDD (n = 26)
Sex, F/M 13/13
Mean onset of disease (range), yr 63.5 (52–77)
Mean duration of disease (range), yr 7.2 (6–11)
Mean age at death (range), yr 70.2 (59–86)

HDDD = hereditary dysphasic disinhibition dementia.