Table 1.
Age (years) | 13.7 ± 2.8 |
Sex (male/female) | 16 (49)/17 (51) |
Exocrine enzyme replacement | 30 (91) |
Genotype | |
Homozygous F508del | 20 (61) |
Heterozygous F508del | 8 (24) |
Other | 3 (9) |
Unknown | 2 (6) |
Age of diagnosis of cystic fibrosis (years) | 0.47 ± 2.0 |
wtSDS | −0.78 ± 1.1 |
Height SDS | −0.41 ± 0.92 |
Change in wtSDS* | −0.16 ± 0.38 |
Change in height SDS* | 0.03 ± 0.24 |
%FEV1 | 85 ± 20 |
%FVC | 94 ± 17 |
Change in %FEV1* | −5 ± 8 |
Change in %FVC* | −3 ± 8 |
Data are n (%) or means ± 1 SD. n = 33.
*Over the preceding year.