Table 2.
Major Criteria |
---|
Beighton score 4/9 or greater (either currently or historically) |
Arthralgia for longer than 3 months in 4 or more joints |
Minor criteria |
Beighton score of 1–3/9 (0–3 if aged 50+) |
Arthralgia in 1–3 joints or back pain or spondylosis, spondylolisthesis |
Dislocation in more than 1 joint, or in 1 joint or more on more than 1 occasion |
Three or more soft tissue lesions (e.g., epicondylitis, tenosynovitis, bursitis) |
Marfanoid habitus (tall, slim, span>height, upper segment : lower segment ratio <0.89, Arachodactyly) |
Skin striae, hyperextensibility, thin skin or abnormal scarring |
Eye signs: drooping eyelids or myopia or antimongoloid slant |
Varicose veins or hernia or uterine/rectal prolapse |
Mitral valve prolapse (by echocardiography) |
|
HMS diagnosis requires |
Two major criteria or |
One major + two minor criteria or |
Four minor criteria or |
Two minor criteria and unequivocally affected first-degree relative |
HMS is excluded by the presence of marfan or Ehlers-Danlos Syndromes.