Table 1.
MD patient | Sex/age (year) | Arm measured | Distribution of dystonia | Distribution of myoclonus | BFMDRS/UMRS | Months since last BTX treatment | Medication |
---|---|---|---|---|---|---|---|
1 | M/49 | R | N, T, WC | N, UL | NAa | 10 | Trihexyphenidyl, paroxetine, phenobarbital, clonazepam |
2 | F/47 | L | N | N, UL | 13/9 | 2 | Atenonol |
3 | F/29 | R | N | N, UL | 17/4 | 2 | – |
4 | M/49 | L | N, UL | Cr, N, UL, LL | 15/20 | 1 | Venlafaxine |
5 | M/65 | R | N | – | 8/3 | 20 | – |
6 | F/45 | R | N, UL | N, UL, LL | NAb | 2 | – |
Cr cranial, N neck, T trunk, LL lower limbs, UL upper limbs, WC Writer’s cramp, BFMDRS Burke Fahn Marsden dystonia rating scale, UMRS Unified myoclonus rating scale, NA not available.
aPatient 1 was more affected with dystonia than myoclonus in the neck.. Myoclonus was also present in the trunk.
bIn Patient 6, the myoclonus in the neck was more pronounced