Table 4. Association Between Patient Characteristics and ADAMTS13 Deficiency Using Multivariate Analysis.
At Least 1 Positive Criterion | All 3 Criteria Positive | |
Sensitivity | 98.8 (96.9–100) | 46.9 (41.3–53.1) |
Specificity | 48.1 (38.9–59.3) | 98.1 (94.4–100) |
Positive predictive value | 85.0 (82.6–87.7) | 98.7 (96.4–100) |
Negative predictive value | 93.3 (85.2–100) | 38.6 (35.8–41.9) |
Abbreviations: ANA, antinuclear antibodies; CI, confidence interval by bootstrap resampling technique.