Table 2.
Baseline Characteristics and Response to Standing, LQT1 Versus LQT2
| LQT1 (n = 31) | LQT2 (n = 28) | p Value | |
|---|---|---|---|
| Age, yrs | 33 ± 15 | 30 ± 13 | 0.400 |
| Female | 21 (68) | 23 (82) | 0.243 |
| Baseline heart rate, beats/min | 67 ± 11 | 62 ± 9 | 0.051 |
| Baseline QT interval, ms | 445 ± 42 | 455 ± 45 | 0.375 |
| Baseline QTc interval, ms | 468 ± 39 | 460 ± 39 | 0.445 |
| Response to standing | |||
| Increment in heart rate, beats/min | 24 ± 10 | 26 ± 11 | 0.474 |
| Maximal heart rate, beats/min | 95 ± 14 | 91 ± 13 | 0.053 |
| Δ QT during maximal tachycardia, ms | −8 ± 32 | 21 ± 28 | 0.001 |
| Δ QTc during maximal tachycardia, ms | 67 ± 41 | 114 ± 42 | <0.001 |
| Δ QTc during longest QT interval, ms | 80 ± 50 | 126 ± 49 | 0.001 |
| Δ QTc during maximal QT interval stretching, ms | 73 ± 43 | 119 ± 48 | <0.001 |
Data are mean ± SD or n (%).
Abbreviations as in Table 1.