Table 1.
Study | Age (years) | Gender | Location | Cutaneous lesion | KMP | Treatment | Outcome |
---|---|---|---|---|---|---|---|
Lai et al. [31] | 2 | Male | Radius/ulna/forearm | Yes | Yes | Amputation, XRT | ANED |
Lyons et al. [34] | 2 | Male | Temporal bone/neck | Yes | No | Excision | ANED |
DeFatta et al. [16] | 3 | Male | Hard palate/soft palate/mucosa/submucosa | Yes | NA | Excision | ANED |
Lalaji et al. [32] | 1 | Female | Temporal bone/lateral mass C1/occipital bone/ear | Yes | Yes | Oral prednisone | Unknown |
Gruman et al. [22] | 2 | Female | Mandible/maxilla/cheek | Yes | No | Interferon α-2b/prednisone | AWD |
Mac-Moune Lai et al. [35] | 5 | Female | Humerus | Yes | NA | Excision | AWD |
KMP = Kasabach-Merritt phenomenon; NA = not available; XRT = radiation therapy; ANED = alive with no evidence of disease; AWD = alive with disease.