FIG. 1.

Computer tomography scans of four patients with LAM. (A) shows numerous, relatively large, thin-walled cysts replacing the normal lungs. Arrow points to the wall of a cyst. (B) shows innumerous small thin-walled cysts distributed throughout the lungs replacing the normal lung parenchyma. (C) shows a large abdominal lymphangioleiomyoma (marked by the asterisk) surrounding the iliac vessels. (D) shows the same tumor surrounding the aorta (A) and inferior vena cava (IVC). (E) shows that lymphangioleiomyomas may appear as fluid-filled cystic structures (box and arrow). (F) shows large angiomyolipomas involving the right (inside box) and left kidneys. The normal kidney anatomy is distorted, making the kidney parenchyma almost completely unrecognizable.