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. Author manuscript; available in PMC: 2011 Jun 1.
Published in final edited form as: Environ Mol Mutagen. 2010 Jun;51(5):360–379. doi: 10.1002/em.20571

Table IV.

Mitochondrial Translation Factors.

Name Official
symbol
Function(s) in Translation Associated Disease Relation
IF2mt MTIF2 Initiation Parkinson's Disease
IF3mt MTIF3 Initiation
Subunit disassociation
EF-Tumt TUFM Delivers aminoacylated
tRNAs
Translation fidelity
Protein folding chaperone
Infantile encephalopathy
EF-Tsmt TSFM Guanine nucleotide
exchange factor for EF-
Tumt
Encephalomyopathy
Hypertrophic cardiomyopathy
EF-G1mt GFM1 Translocation Infantile encephalopathy
Early-onset Leigh syndrome
Progressive hepatoencephalopathy
EF-G2mt GFM2 Ribosome recycling
mtRRF MRRF Ribosome disassembly
mtRF1 MTRF1 Translation termination?
mtRF1a MTRF1L Translation termination
HHS Vulnerability Disclosure