Table 2.

Clinical presentation of the Iranian DFNB2 family L-1419

Patient	Age	Sex	Onset of hearing loss	Hearing threshold (dB)	Caloric test	Fundus examination	Visual acuity
V:1	39	M	Seven months	≥ 70	Normal	Normal	20/20
V:2	31	M	7 years	≥ 45	Not tested	Normal	20/20
V:3	42	F	1.5 years	≥ 70	Normal	Normal	20/20